Raynaud's phenomenon in pediatric age

Results Sixty six cases (71,2% female) met the inclusion criteria. Average age of RP onset was 12,5y with median duration of 3,6y. RP was associated to: erythema pernio (34,8%), inter-phalangeal joints pain (30.3%), hands edema (28,8%), acrocyanosis (18,2%), profuse sweating (12,1% ) and trophic changes of fingers pulp (10,6%.). Antinuclear antibodies (ANA) were titled in 64 patients (97%), being positive (>1/80) in ten (15.6%). Capillaroscopy was performed on 43 (65.2%): 32 (74,4%) minor changes (tortuosity and segmental enlargement), four (9,3%) significant changes (giant capillaries, hemorrhagic and avascular areas), seven (16,3%) normal. Of 43 patients with complete study, five (11,6%) had secondary RP: two with juvenile systemic sclerosis, two in characterization and a probable case of mixed connective tissue disease. Secondary RP occurred mostly in less that 12-yearsold child. ANA ≥ 1/320 and significant changes on capillaroscopy had a significant statistic relationship with secondary RP.